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Clinical Neurology 2019-Nov

[A women with aplastic anemia developed chronic inflammatory demyelinating polyneuropathy].

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Masaaki Abe
Fumitaka Shimizu
Munehisa Suzukawa
Toshihiko Maeda
Masatoshi Omoto
Takashi Kanda

Ključne riječi

Sažetak

A 66-year-old female developed chronic inflammatory demyelinating polyneuropathy (CIDP) one year after the diagnosis of aplastic anemia. High-dose intravenous immunoglobulin (IVIg) therapy, followed by IVIg maintenance therapy, rapidly improved her weakness and hyperesthesia in four extremities. In addition, pancytopenia caused by aplastic anemia also improved following IVIg treatment in parallel. This is the first report to show the co-existence of CIDP and aplastic anemia, and a common pathomechanism may be present in these two rare autoimmune disorders.

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