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pulmonary veno-occlusive disease/kalij

Veza se sprema u međuspremnik
ČlanciKliničkim ispitivanjimaPatenti
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[Eisenmenger's syndrome. Advances in pathobiology and treatment].

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The term Eisenmenger Syndrome is used to refer to any systemic to pulmonary congenital communication causing pulmonary vascular obstructive disease (PVOD) severe enough as to produce bidirectional or reversed shunt. Once established, the PVOD deteriorates the quality of life and limits the survival

Genetics of pulmonary hypertension.

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OBJECTIVE The identification of the genetic basis for heritable predisposition to pulmonary arterial hypertension (PAH) has altered the clinical and research landscape for PAH patients and their care providers. This review aims to describe the genetic discoveries and their impact on clinical

Genetics of pulmonary hypertension in the clinic.

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Heritable pulmonary arterial hypertension (PAH) is an autosomal dominant disease with incomplete penetrance because of mutations in bone morphogenetic protein receptor-II (BMPR2), activin A receptor type II-like kinase 1, endoglin, caveolin-1, potassium channel subfamily K, member 3, and T-box gene
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