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pulmonary veno-occlusive disease/umor

Veza se sprema u međuspremnik
ČlanciKliničkim ispitivanjimaPatenti
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Pulmonary veno-occlusive disease, antiphospholipid antibody and pulmonary hypertension in an adolescent.

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Pulmonary veno-occlusive disease (PVOD) is a rare cause of pulmonary hypertension (PH); Antiphospholipid antibody (APL) is another known cause of pulmonary hypertension, due to recurrent pulmonary thromboembolism. The coincidence of both causes, PVOD and APL, without thromboembolism, in PH has not
OBJECTIVE To deepen our understanding of Methylmalonic aciduria (MMA) associated pulmonary hypertension (PH) by analyzing the characteristics of clinical presentation, pulmonary high resolusion CT(HRCT), treatment response and gene mutation. METHODS This study includes 15 cases of pediatric patients
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