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Medycyna wieku rozwojowego

[Takayasu's disease in a 14 years old girl].

Ní féidir ach le húsáideoirí cláraithe ailt a aistriú
Logáil Isteach / Cláraigh
Sábháiltear an nasc chuig an gearrthaisce
Maria Korzon
Wiesława Bukowska
Aldona Kotłowska-Kmieć
Barbara Kamińska

Keywords

Coimriú

Takayasu's disease is a chronic, nonspecific arteritis of unknown etiology. It mainly affects young women in the second and third decade of life. The reports of the disease in pediatric patients are rare. The pathological process involves all the layers of the arterial wall. It affects primarily the aortic arch and its main branches. If the renal arteries are involved, hypertension develops. A 14-year-old girl suffered from Takayasu's disease was described. The first symptoms: tonic-clonic seizures, neurological signs and high arterial blood pressure were observed in a previously healthy girl. The diagnostics process was presented with special attention given to the interpretation of radiological imagings. The diagnosis of Takayasu's disease was based on result of angiography. This examination demonstrated the abdominal aorta abnormalities which have been described in patients with Takayasu's disease and the right renal artery stenosis.

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