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polyarteritis nodosa/protease

Veza se sprema u međuspremnik
ČlanciKlinička ispitivanjaPatenti
5 rezultatima
OBJECTIVE Assessment of the value of determination of antineutrophil cytoplasmic antibodies (ANCA) and its specificities for classification of patients with biopsy-proven necrotizing arteritis. METHODS The serum samples of 28 consecutive patients with biopsy-proven vasculitis involving medium-

Thrombotic thrombocytopenic purpura associated with polyarteritis nodosa.

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Prijava Registriraj se
We present a case of classical polyarteritis nodosa (PN) overlapping thrombotic thrombocytopenic purpura (TTP). A 70-year-old woman was transferred to our hospital because of general fatigue and fever. On admission, laboratory findings revealed leukocytosis, normochromic normocytic anemia and renal

Primary systemic vasculitis with severe α1-antitrypsin deficiency revisited.

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Prijava Registriraj se
OBJECTIVE To study the clinical characteristics and epidemiology of the combination of primary systemic vasculitis (PSV) and severe alpha-1 antitrypsin (α1-AT) deficiency. METHODS Patients with PSV [granulomatosis with polyangiitis (GPA) (Wegener's), microscopic polyangiitis, eosinophilic

[Vasculitis of the kidney].

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Prijava Registriraj se
Panarteritis nodosa, Wegener's granulomatosis and idiopathic necrotizing glomerulonephritis, regarded by some as a vasculitis restricted to the glomerulus, are those forms of primary vasculitis most often encountered in renal biopsy. The histopathologic differential diagnosis can be difficult and

Antineutrophil cytoplasmic antibodies: a still-growing class of autoantibodies in inflammatory disorders.

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Prijava Registriraj se
Antineutrophil cytoplasmic antibodies (ANCA) have been described as sensitive and specific markers for active Wegener's granulomatosis (WG). ANCA in WG produce a characteristic cytoplasmic staining pattern of neutrophils (c-ANCA) and are directed against proteinase 3 (Pr3), a serine protease from
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