Hereditary angioedema (HAE) is a disorder that results in recurrent attacks of severe swelling. The swelling most commonly affects the arms, legs, face, intestinal tract, and airway and is usually not itchy. If the intestinal tract is affected, abdominal pain and vomiting may occur. Swelling of the airway can result in its obstruction. Without preventive treatment, attacks typically occur every two weeks and last for a few days.There are three main types of HAE. Types I and II are caused by a mutation ...
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