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International Journal of Cardiology 2007-Jun

Fibrosing mediastinitis presenting as pulmonary stenosis: stenting works.

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Ruby Satpathy
Virginia Aguila
Syed M Mohiuddin
Ijaz A Khan

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Abstrè

A rare case of fibrosing mediastinitis from histoplasmosis with extrinsic compression of the right pulmonary artery is reported. A 41-year-old patient presented with worsening symptoms of cough, fever, migratory arthralgia, chest pain, and progressive dyspnea. The pulmonary artery involvement was suspected by transthoracic echo and was confirmed by transesophageal echo, CT scan of chest, and right heart catheterization. Diagnosis of histoplasmosis was confirmed by biopsy and serological tests. Patient has been free from symptoms of pulmonary stenosis for 4 years after successful pulmonary artery stenting.

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