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BMJ Case Reports 2020-Jul

Pulmonary mucinous cystadenocarcinoma: an unusual presentation and literature review

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Pandi Todhe
Nishant Sharma
Ajay Shetty
Pius Ochieng

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Cystic lung disease is a group of heterogeneous pulmonary diseases resulting from hereditary/congenital disorders, systemic disorders and infectious causes among others. Pulmonary mucinous cystic neoplasia is a spectrum of neoplastic cystic diseases with abundant mucin, of which pulmonary mucinous cystadenocarcinoma (PMC) is a rare malignant subtype. We present a case of a 66-year-old man who presented with dyspnoea, cough, fatigue and weight loss. Imaging of his chest showed numerous cavitary lesions, and the diagnosis of PMC was made based on lung biopsy. He received palliative chemotherapy and died 1 year later. We present a literature review of PMC based on 26 reported cases, including our own.

Keywords: lung cancer (oncology); surgical oncology; tobacco related disease.

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