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Radiology 2015-Dec

Case 224: Cardiac Involvement in Erdheim-Chester Disease.

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Krækjan er vistuð á klemmuspjaldið
Jaime de Miguel Criado
Luis F Aguilera Del Hoyo
Laura García Del Salto
Eva Cueva Pérez
Jesús Casado Cerrada
Santiago Nieto Llanos
José Carlos Porro Fernández
Patricia Fraga Rivas

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Útdráttur

History A 61-year-old man with no relevant medical history was admitted to the emergency department with symptoms of congestive heart failure and a 1-week history of chest pain, progressive dyspnea, abdominal swelling, bipedal edema, and anorexia. Laboratory test results, including complete blood count and electrolyte, creatinine, creatine phosphokinase, and troponin T levels were normal. Electrocardiographic findings were unremarkable. Initial chest radiography showed an enlarged heart with bilateral pleural effusion. Transthoracic echocardiography revealed an irregular right atrial mass and moderate to severe pericardial effusion. The patient subsequently underwent computed tomography (CT) of the chest, abdomen, and pelvis followed by cardiac magnetic resonance (MR) imaging for further evaluation of the atrial mass. Because of the suspected diagnosis, conventional radiography of the skeleton was performed.

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