Ophthalmic Surgery Lasers and Imaging Retina 2014-Jan
Parry-Romberg syndrome studied by spectral-domain optical coherence tomography.
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Parry-Romberg syndrome is a rare disorder characterized by progressive hemifacial atrophy. Ophthalmic findings are characterized by enophthalmos, strabismus, nerve palsies, anisometropia, glaucoma, and angle abnormalities. Vision loss has also been reported due to retinal changes such as venous dilatation, disc edema, retinal edema, and retinal folds. The authors describe a case of Parry-Romberg syndrome with retinal alterations but a normal macula on spectral-domain optical coherence tomography.