Nephrologie & therapeutique 2012-Dec
[Renal vein infarction, a complication of paroxysmal nocturnal hemoglobinuria].
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Krækjan er vistuð á klemmuspjaldið
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Útdráttur
Paroxysmal nocturnal hemoglobinuria (Marchiafava-Micheli disease) is a rare acquired clonal disorder of the hematopoietic cell, to a somatic mutation in the phosphatidylinositol glycan (PIG-A). The most frequent clinical manifestations are hemolytic crisis and venous thrombosis of the mesenteric, hepatic, portal or cerebral territories. We report a case of paroxysmal nocturnal hemoglobinuria with renal vein thrombosis, a rare complication of this disease.