Neurothekeoma is a benign cutaneous tumor first described by Gallager and Helwig, who proposed the term in order to reflect the presumed origin of the lesion from nerve sheath. Microscopically, the lesions described closely resembled the tumor, 'nerve sheath myxoma', an entity first described by Harkin and Reed. The latter had, through the years, been variously described as 'Bizarre cutaneous neurofibroma', 'Myxoma of nerve sheath', and 'Pacinian neurofibroma'.Clinically, neurothekeomas present as ...
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