Indian Pediatrics 2014-Nov
Severe calcinosis cutis with cutaneous ulceration in juvenile dermatomyositis.
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概要
BACKGROUND
Calcinosis cutis is usually seen in long standing and untreated cases of juvenile dermatomyositis.
METHODS
7-year-old girl with severe calcinosis cutis who developed cutaneous ulceration, rash and myopathy.
METHODS
Myopathic changes in EMG, muscle edema in MRI, elevated muscle enzymes and Jo-1 positive antibodies.
RESULTS
Treatment with prednisolone and methotrexate resulted in improvement of the lesion.
CONCLUSIONS
Calcinosis cutis may be a presenting feature of juvenile dermatomyositis even in the absence of characteristic findings of rash and weakness.