British Journal of Oral and Maxillofacial Surgery 2010-Apr
Tuberous sclerosis with oral angiofibroma: case report.
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概要
Tuberous sclerosis is a multisystem disorder characterised by the formation of hamartomas in various parts of the body. We present a patient who presented with facial angiofibromas (adenoma sebaceum), shagreen patches, and epileptic seizures. Oral papules showed histological features of angiofibroma, which was peculiar to this case.