OBJECTIVE
To describe the aetiology, clinical features and appropriate treatment for hepatic glycogenosis in poorly controlled type 1 diabetes.
METHODS
A review of three adolescents with poor diabetes control, hepatomegaly and elevated serum liver transaminase concentrations.
RESULTS
Symptoms
In adults with diabetes mellitus, hepatomegaly and abnormalities of liver enzymes occur as a consequence of hepatocellular glycogen accumulation, as has been well described in children. During periods of hyperglycemia glucose freely enters the hepatocytes driving glycogen synthesis, which is