Ectopia cordis (Greek: 'away / out of place' + Latin: 'heart') or ectopic heart is a congenital malformation in which the heart is abnormally located either partially or totally outside of the thorax. The ectopic heart can be found along a spectrum of anatomical locations, including the neck, chest, or abdomen. In most cases, the heart protrudes outside the chest through a split sternum.
Ectopia cordis results from a failure of proper maturation of midline mesoderm and ventral body wall formation ...
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