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International Journal of Surgery Case Reports 2015

Calvarial ectopic meningothelial meningioma.

Samo registrirani uporabniki lahko prevajajo članke
Prijava / prijava
Povezava se shrani v odložišče
Roberto Bezerra Vital
Pedro Tadao Hamamoto Filho
Renan Luiz Lapate
Vinícius Zanin Martins
Flávio de Oliveira Lima
Flávio Ramalho Romero
Marco Antônio Zanini

Ključne besede

Povzetek

BACKGROUND

Meningiomas are the most common benign neoplasm of the brain whereas ectopic presentation, although reported, is rare. Among these ectopic tumors, there are a group of purely intraosseous meningiomas, which usually are diagnosed differentially from common primary osseous tumor such as fibrous dysplasia and osteoid osteoma.

METHODS

We report a 62-year-old female with a history of headaches and 6 months of progressive right parietal bulging, with no neurological signs. Parietal craniotomy was performed with immediate titanium cranioplasty of the parietal convexity. Histopathology exams revealed an ectopic intradiploic meningioma without invasion of cortical layers, with positive staining for progesterone receptors and epithelial membrane antigen.

CONCLUSIONS

Ectopic intraosseous meningiomas remain a rare neoplasm with only a few cases reported. The main theories to justify the unusual topography appear to be embryological remains of neuroectodermal tissue or cellular dedifferentiation. Surgical treatment seems the best curative option.

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