[Hypertrophic osteoarthropathy in congenital cyanotic cardiopathy, description of 2 cases].
Ključne besede
Povzetek
Hypertrophical osteortropathy syndrome, which consists of arthritis, periostitis, growth of the periarticular soft tissue and fingers like drumsticks, is associated to several cardiopulmonary sufferings, its relation to cyanotic congenital cardiopathies has been rarely informed. Two cases of this rare association are described in this article, and the possible patogenic mechanisms are discussed. To distinguish this syndrome from other rheumatic sufferings such as Rheumatic Fever, Juvenile Rheumatoide Arthritis or Gout is an important point, because its treatment and prognostic are different.