Prune belly syndrome is a rare, genetic birth defect affecting about 1 in 40,000 births. About 97% of those affected are male. Prune belly syndrome is a congenital disorder of the urinary system, characterized by a triad of symptoms. The syndrome is named for the mass of wrinkled skin that is often (but not always) present on the abdomen of those with the disorder.
Prune-belly triad consists of: Cryptorchidism, abdominal wall defects and genitourinary defects:
A partial or complete lack of abdominal ...
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* All information baseras på publicerad vetenskaplig forskning