Neuronal ceroid lipofuscinosis is the general name for a family of at least eight genetically separate neurodegenerative lysosomal storage diseases that result from excessive accumulation of lipopigments (lipofuscin) in the body's tissues. These lipopigments are made up of fats and proteins. Their name comes from the word stem 'lipo-', which is a variation on [lipid]], and from the term 'pigment', used because the substances take on a greenish-yellow color when viewed under an ultraviolet light ...
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