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Annali Italiani di Chirurgia 2017-Jan

Giant retroperitoneal dedifferentiated liposarcoma.

Watumiaji waliosajiliwa tu ndio wanaweza kutafsiri nakala
Ingia / Ingia
Kiungo kimehifadhiwa kwenye clipboard
Kemal Beksac
Bulent Aksel
Fisun Ardic Yukruk
Olcay Kandemir

Maneno muhimu

Kikemikali

BACKGROUND

Liposarcoma is the most frequent type of retroperitoneal sarcomas. Dedifferentiated liposarcoma is the least common subtype and is an extremely rare tumor.

METHODS

We present the case of a 53-year-old male who was referred with a giant retroperitoneal mass. The patients' mass was deemed unresectable by the previous institution and received chemotherapy with no benefit. We macroscopically removed the 38x32 cm mass with right nefrectomy. Pathological examination revealed dedifferentiated liposarcoma.

CONCLUSIONS

Surgery is the gold standart in the treatment of retroperitoneal sarcomas. Giant masses present a challenge for the surgeon with possible major vascular injuries and multiorgan resections. Therefore it is important for these patients to be referred for surgery without delay.

UNASSIGNED

Dedifferentiated liposarcoma, Liposarcoma, Retroperitoneal sarcoma.

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