Minerva Pediatrica 1992-Nov
[Neonatal hemorrhagic syndrome with unfavorable prognosis].
Watumiaji waliosajiliwa tu ndio wanaweza kutafsiri nakala
Ingia / Ingia
Kiungo kimehifadhiwa kwenye clipboard
Maneno muhimu
Kikemikali
The Authors describe a case of neonatal hemorrhagic syndrome associated with a large hemangioma on the left lower limb with an unfavourable prognosis. The clinical, biohumoral and anatomicopathological characteristics indicate a Kasabach-Merrit syndrome (SKM) with massive platelet sequestration in the large hemangioma. The pathogenetical mechanisms of SKM and the medical surgical and radiant therapy are mentioned. The Authors also discuss the various diagnostic problems imposed by the presence of serious hemorrhagic pathology at neonatal age.