StatPearls Publishing 2019-01
Protein S Deficiency
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Ingia / Ingia
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Protein S deficiency is a rare disorder, characterized by reduced activity of protein S, a plasma serine protease with complex roles in coagulation, inflammation, and apoptosis.[1] A deficiency in protein S characteristically demonstrates the inability to control coagulation, resulting in the excessive formation of blood clots (thrombophilia).