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acne conglobata/protease

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NakalaMajaribio ya klinikiHati miliki
1 matokeo

[Pyroderma fistulans sinifica associated with congenital alpha-1-antitrypsin deficiency].

Watumiaji waliosajiliwa tu ndio wanaweza kutafsiri nakala
Ingia / Ingia
A patient is reported who suffered from pyodermia fistulans sinifica (acne conglobata sinifica, acne tetrade) and who presented a severe congenital alpha-1-antitrypsin deficiency (phenotype ZZ). The possible significance of the protease inhibitor deficiency for the development of this disease is
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