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factor xi deficiency/tyrosine

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NakalaMajaribio ya klinikiHati miliki
2 matokeo

Disruption of disulfide bonds is responsible for impaired secretion in human complement factor H deficiency.

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Ingia / Ingia
Factor H, a secretory glycoprotein composed of 20 short consensus repeat modules, is an inhibitor of the complement system. Previous studies of inherited factor H deficiency revealed single amino acid substitutions at conserved cysteine residues, on one allele arginine for cysteine 518 (C518R) and

The susceptibility of plasma coagulation factor XI to nitration and peroxynitrite action.

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Ingia / Ingia
Coagulation factor XI is present in blood plasma as the zymogen, like other serine proteases of hemostatic system, but as the only coagulation factor forms 140-160kDa homodimers. Its activation is induced by thrombin, and a positive feedback increases the generation of the extra thrombin.
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