[Cerebrovascular disorders in young patients with livedo racemosa generalisata (Ehrmann)].
Anahtar kelimeler
Öz
The results of examinations on 15 patients suffering from livedo racemosa generalisata (idiopathic livedo reticularis) are described. 12 of the patients were found to have cerebrovascular disturbances (in most cases severe) and 2 of them had migraine accompagnée. The remaining patient had no neurological changes. The majority of the patients were women (12 female, 3 male). In most cases the illness began between the age of 20 and 30 years. Cerebral angiographic examinations showed the existence of peripheral angiostenosis, whereas in 9 patients pronounced cases of diffused cerebral atrophy could be found with the help of computerised tomography. Questions concerning the nosological position, pathogenesis and therapy of livedo racemosa generalisata are discussed.