Juvenile xanthogranuloma is a form of histiocytosis, classified as 'non-Langerhans cell histiocytosis', or more specifically, 'type 2'.It is a rare skin disorder that primarily affects children under one year of age but can also be found in older children and adults. It was first described in 1905 by Adamson. In 5% to 17% of people, the disorder is present at birth, but the median age of onset is two years. JXG is a benign idiopathic cutaneous granulomatous tumor and the most common form of non-Langerhans ...
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