American Journal of Obstetrics and Gynecology 2004-Feb
Embryonal sarcoma of the liver in pregnancy, associated with HELLP syndrome.
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After cesarean section, a 30-year-old patient with HELLP syndrome (hemolysis, elevated liver enzymes, and low platelet count in association with preeclampsia) had fever, jaundice, loss of ascites, and a cardiac murmur. Magnetic resonance imaging showed a tumor extending from the left lobe of the liver into the inferior vena cava, right atrium, and ventricle. The biopsy specimen revealed an embryonal sarcoma of the liver. On the second day of chemotherapy, the patient died of intra-abdominal hemorrhage from the tumor.