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JPMA. The Journal of the Pakistan Medical Association 2008-Nov

Kikuchi-Fujimoto Disease presenting with fever, lymphadenopathy and dysphagia.

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A K M Mosharraf-Hossain
Pran Gopal Datta
A S Ahmed Amin
M Jalal Uddin

关键词

抽象

Kikuchi Fujimoto Disease (KFD) can present with dysphasia, fever and lymphadenopathy. A young Bangladeshi girl presented with fever, cervical lymphadenopathy, dysphasia, weight loss and skin rash. Antitubercular drugs were given on clinical judgement, with no improvement after one month. Later, fine needle aspiration and histopathology of Lymph Node suggested KFD. Computerized Tomography (CT) scan of neck revealed enlarged retropharyngeal lymphnode (LN) causing pharyngeal narrowing. Oral Prednisolone was given showing improvement and no relapse was encountered. KFD may present with dysphasia uncommonly along with fever and lymphadenopathy. Awareness of this disorder by clinicians and pathologists will help prevent misdiagnosis and inappropriate treatment.

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