Pediatric Emergency Care 2009-May
Moyamoya disease in an 8-year-old boy presenting with weakness.
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Moyamoya disease is a progressive, unilateral, or bilateral carotid artery stenosis of unknown etiology. It often presents in children as a transient ischemic attack, with a focal neurological deficit. This case describes an 8-year-old boy who presented with left-sided weakness secondary to moyamoya vasculopathy.