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Arquivos Brasileiros de Oftalmologia

Retinal vasculitis in Susac syndrome: case report.

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Gherusa Helena Milbratz
Francisco Azevedo Marquardt
Heriberto Pinto Guimarães Neto
Daniel Azevedo Marquardt
Eduardo Soares Maia Vieira de Souza

关键词

抽象

A 29 year old male was admitted at the emergency room suffering from gradually worsening headache followed by nausea. In the hospital patient presented with lethargy, reduction of consciousness level and bilateral hypoacusis. Ophthalmic examination and fluorescein angiography showed retinal vasculitis. This finding was crucial to the diagnosis of Susac syndrome, a rare disease characterized by vasculopathy of retina, encephalic tissues and cochlea. Patient was treated with immunosuppressors to prevent him from developing severe sequelae of this disease.

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